MAYER-ROKITANSKI-KUSTER-HAUSER SINDROMI BOR AYOLLARDA BACHON MIOMASI (Klinik holat)
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Mayer Rokitanskiy-Kuster-Hauzer sindromi, bachadon miomasi, rudimentar bachadon, laparoskopiya, klinik holat##article.abstract##
Mayer-Rokitanskiy-Küster-Hauzer sindromi - bu reproduktiv, buyrak, suyak va yurak nuqsonlarini o'z ichiga olgan tug'ma kasallik. Kasallik 4000-5000 tirik tug'ilgan ayoldan 1 tasini tashkil qiladi. Fenotipi ayol, karyotip 46 XX, odatda rivojlangan ikkilamchi jinsiy belgilar va funktsional tuxumdonlar. MRKXSda bachadon qoldiqlaridan miomalarning paydo bo'lishi juda kam uchraydi, garchi adabiyotda bir nechta holatlar qayd etilgan. Bu holatda tashxis qo'yish va davolashga yondashuv juda murakkab. Bu erda biz MRKXS bilan og'rigan 30 yoshli ayolning oddiy bachadon miomasi borligi aniqlangan klinik holatini taqdim etamiz.
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