MAYER-ROKITANSKIY-KUSTER-XAUZER SINDROMI BO’LGAN BEMORLARDA IKKILANGAN RUDIMENTAR BACHADONLARNING KLINIK VA EXOGRAFIK XUSUSIYATLARI
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birlamchi amenoreya, ultratovush tekshiruvi, magnit-rezonans tomografiya, funksional neovagina##article.abstract##
Mayer–Rokitanskiy–Kustner–Xauzer sindromi tug'ma anomaliya bo'lib, normal 46XX kariotipi va saqlanib qolgan tuxumdon funktsiyasi bilan bachadon va yuqori qinning yo'qligi yoki rivojlanmaganligi bilan tavsiflanadi. Kasallik o'smir qizlarda birlamchi amenoreyaning asosiy sabablaridan biridir. Klinik jihatdan, bu ikkilamchi jinsiy xususiyatlarning normal rivojlanishi va hayz ko'rishning yo'qligi bilan namoyon bo'ladi. Tashxis ultratovush, MRT va klinik tekshiruv ma'lumotlariga asoslanadi. Davolashning asosiy yo'nalishi funktsional neovagina yaratish, shuningdek, psixosotsial yordam ko'rsatishdir.15 yoshdan 25 yoshgacha bo'lgan bachadon va qin nuqsonlari bo'lgan 20 nafar qiz tekshirildi. Barcha bemorlar klinik tekshiruvdan o'tdilar, shu jumladan anamnestik ma'lumotlar, ginekologik tekshiruv, ultratovush tekshiruvi va jarrohlik amaliyoti, so'ngra exografik nazorat o’tkazildi.
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